Function of carnitine in the transport of mitochondrial long chain Download Scientific Diagram l carnitine: Nutrition, pathology, and health benefits ScienceDirect Carnitine is an essential cofactor for transport of long chain fatty acids into mitochondria, where oxidation takes place. Carnitine deficiency leads to depressed mitochondrial oxidation of fatty acids, resulting in storage of fat The Role of l Carnitine in Mitochondria, Prevention of Metabolic Inflexibility and Disease Initiation Carnitines as Mitochondrial Modulators of Oocyte and Embryo Bioenergetics The Role of l Carnitine in Mitochondria, Prevention of Metabolic Inflexibility and Disease Initiation